A
powdered medical food containing a mixture of
pure L-amino acids free from methionine and enriched with
vitamins, minerals, and trace elements. For the dietary
management of vitamin B6 non-responsive homocystinuria
in children and adults, including pregnant women and women
of child-bearing age.
Enriched with vitamins, minerals and trace elements
Osmolality
(at a 1 to 9 dilution): 810 mOsm/kg
Indications:
Homocystinuria - vitamin B6 non-responsive (due to Cystathionine ß-Synthase
Deficiency)
Directions for Preparation and Use:
The amount of HOM 2 needed
to supplement total daily protein requirements (other than
methionine) depends on age, body weight and individual methionine
tolerance. The dose of HOM 2 must be determined
by a physician or dietitian and adjusted periodically. Diets
with HOM 2 must contain adequate amounts of energy, essential
fatty acids and methionine to meet daily requirements.
The daily amount required should be divided into 3 to 5 single
portions and can be taken mixed with calculated amounts of
other food (e.g. beverages, fruit mousse). For accuracy, HOM
2 should be weighed on a gram scale.
Household
Measurement
g
Product
g
Protein
1
Tablespoon
9
6
1/4
Cup
37
24
1/3
Cup
50
35
1/2
Cup
82
55
1
Cup
161
110
69
g Protein per 100 g Product
Precaution:
Not suitable as a sole source of nutrition
Not for parenteral
use
Storage:
Store unopened cans at room temperature. Do not store at
extreme temperatures. After opening, keep can tightly covered
and store in a cool, dry place (not in the refrigerator)
and use within four weeks.
Metabolics
