This formulation is available in the US and Canada.
Main Features:
Lysine-
and tryptophan-free unflavored powder
Contains
a balanced mixture of all other essential and non-essential
amino acids, carbohydrate, fat, vitamins, minerals and trace
elements (including iron, selenium and chromium)
XLys,
XTrp Analog provides 13 g of protein equivalent per 100
g of powder
Osmolality
(at 15% w/v) = 377 mOsm/kg
Indications:
Glutaric
acidemia type I
Directions for Preparation and Use:
Analog metabolic infant formulas must be consumed in conjunction
with a whole protein source (e.g. breast milk or standard
infant formula) in quantities prescribed by a dietitian
or physician to meet complete protein requirements and ensure
normal growth.
Formula
dosage will vary depending on the age, body weight, medical
condition and protein tolerance of the infant.
Boil
water for 5 minutes and allow to cool for at least 30 minutes
so that it feels warm to the wrist.
Add
the prescribed amount of Analog powder and a protein
source to the sterilized feeding bottle. For accuracy, Analog should be weighed on a gram scale. If using the provided scoop,
fill it and level off with a clean, dry knife. Do not press
the powder into the scoop.
Pour
the required amount of cooled, boiled water into feeding bottle.
To make the recommended dilution (21 kcal/oz), Analog requires 1 fl oz (30 mL) of water for every 5 g (1 unpacked,
level scoop) of powder. Place cap on bottle and shake until
powder has dissolved.
Make
sure the formula is lukewarm by placing a few drops on your
wrist.
Formula
prepared in advance must be cooled rapidly, stored in the refrigerator
(35°F to 40°F) and used within 24 hours of preparation. Shake
immediately before use. Formula remaining in the bottle after
one hour of feeding should be discarded. Tube feeding "hang
time" should not exceed 4 hours.
Precaution:
Must
only be consumed by infants with proven glutaric acidemia type
1 while under strict medical supervision. Not suitable as a
sole source of nutrition. Not for parenteral use.
Storage:
Store
unopened can at room temperature. Do not store at extreme
temperatures. Once opened, reseal can and store in a cool,
dry place (not in refrigerator) and use within one month.
Metabolics
